Abstract： Leg length discrepancy has remained a great challenge for pediatric orthopedic surgeons. Its major symptoms include lameness, back pain, hip dysplasia and scoliosis. Conventional limb lengthening with an external fixator is associated with joint stiffness, muscle contracture, pin site infection and uncomfortable experiences. Currently intramedullary limb lengthening has become a valuable alternative to external fixation so as to eliminate clinical dependence on external fixation and minimize complications. This review summarized clinical experiences of intramedullary lengthening for providing references for correcting lower limb deformity in children.