Abstract： This article reports a case of autosomal dominant optic atrophy to provide a reference for the clinical diagnosis of this type of disease.The patient had poor vision in both eyes without any obvious cause,and was diagnosed with autosomal dominant optic atrophy after combining auxiliary examinations and genetic testing.There is currently no effective treatment for this disease,and the key to treatment is to improve the patient's visual quality.Lifestyle changes and regular follow-up examinations are usually recommended.